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Pathways of ammonia detoxification to GLN in muscles connected with enhanced use with the BCAA and α-KG (cataplerosis) and instructed results of BCAA and phenylbutyrate in topics with liver cirrhosis or UCD. Beneficial result of BCAA on ammonia detoxification to GLN could be blunted by GLN degradation to ammonia in enterocytes and kidneys. Phenylb